| Condition | Symptoms | Answer | % Correct |
|---|---|---|---|
| leukemia | auer rods | AML | 60%
|
| leukemia | philadelphia chromosome | CML | 60%
|
| thrombocytopenia | ADAMSTS1 antibody | TTP | 60%
|
| leukemia | MC childhood malignancy | ALL | 40%
|
| leukemia | overproliferation of mature lymphocytes | CLL | 40%
|
| leukemia | 9-22 chromosomal translocation | CML | 40%
|
| anemia | fava beans, dapsone, primaquine | G6PD deficiency | 40%
|
| anemia | HFE protein mutation | hemochromatosis | 40%
|
| anemia | bronze skin, DM, cardiomyopathy, hypogonadism, erectile dysfunction | hemochromatosis | 40%
|
| hemophilia | hemarthrosis | hemophilia | 40%
|
| hemophilia | factor 8 deficiency | hemophilia A | 40%
|
| hemophilia | factor 9 deficiency | hemophilia B | 40%
|
| lymphoma | painful LAD after alcohol consumption | Hodgkins lymphoma | 40%
|
| lymphoma | associated w/ EBV | Hodgkins lymphoma | 40%
|
| myeloma | preleukemic disorder that may progress to AML | myelodysplasia | 40%
|
| anemia | autoimmune destruction of intrinsic-factor producing parietal cells | pernicious anemia | 40%
|
| anemia | vasocclusive crisis | sickle cell anemia | 40%
|
| thrombocytopenia | post-viral infection | TTP | 40%
|
| thrombocytopenia | isolated PLT defect | TTP | 40%
|
| anemia | hypersegmented neutrophils, macroovalocytes (2) | vitamin B12 and B9 deficiency | 40%
|
| leukemia | hypercellular bone marrow w/ > 20% blasts | ALL | 20%
|
| anemia | thalassemia MC in east asians | alpha thalassemia | 20%
|
| anemia | heinz bodies (2) | alpha thalassemia, G6PD deficiency | 20%
|
| anemia | increased hepcidin and ferritin, decreased serum iron and TIBC | anemia of chronic disease | 20%
|
| anemia | thalassemia MC in meditteraneans | beta thalassemia | 20%
|
| lymphoma | mandibular/maxillary mass | burkitt's lymphoma | 20%
|
| lymphoma | EBV endemic to South Africa | burkitt's lymphoma | 20%
|
| lymphoma | starry sky appearance on histology | burkitt's lymphoma | 20%
|
| lymphoma | aggressive subtype of nonhodkins lymphoma | burkitt's lymphoma | 20%
|
| leukemia | leukemia cutis | CLL | 20%
|
| leukemia | smudge cells | CLL | 20%
|
| leukemia | treated w/ tyrosine kinase inhibitors | CML | 20%
|
| thrombocytopenia | elevated d-dimer | DIC | 20%
|
| anemia | absorbed in jejunum | folic acid deficiency | 20%
|
| anemia | episodic hemolytic anemia | G6PD deficiency | 20%
|
| anemia | jaundice | G6PD deficiency | 20%
|
| anemia | x-linked disorder (3) | G6PD deficiency, hemophilia A, hemophilia B | 20%
|
| anemia | schistocytes (bite cells) (2) | G6PD deficiency, TTP | 20%
|
| anemia | decreased hepcidin, increased hemosiderin | hemochromatosis | 20%
|
| blood disorder | autosomal recessive disorder (3) | hemochromatosis, hemophilia A, hemophilia B | 20%
|
| hemophilia | christmas disease | hemophilia B | 20%
|
| lymphoma | painless cervical/supraclavicular LAD(firm, nontender, freely mobile) | Hodgkins lymphoma | 20%
|
| lymphoma | contiguous spread through upper body LN | Hodgkins lymphoma | 20%
|
| lymphoma | pel-ebstein (cyclical) fever | Hodgkins lymphoma | 20%
|
| lymphoma | nodular sclerosis MC type | Hodgkins lymphoma | 20%
|
| lymphoma | reed sternburg cells (bilobular nucleus) | Hodgkins lymphoma | 20%
|
| anemia | pica, pagophagia, koilonychia | iron deficiency anemia | 20%
|
| myeloma | bence jones proteins | multiple myeloma | 20%
|
| myeloma | bone pain (spine/rib), recurrent infection, elevated calcium, anemia, kidney failure | multiple myeloma | 20%
|
| myeloma | punched out lytic lesions on skull XRAY | multiple myeloma | 20%
|
| myeloma | roleaux formation | multiple myeloma | 20%
|
| myeloma | > 20% myeloblasts on bone marrow biopsy | myelodysplasia | 20%
|
| lymphoma | painless peripheral LAD | non Hodgkins lymphoma | 20%
|
| lymphoma | extranodal spread to GI tract | non Hodgkins lymphoma | 20%
|
| lymphoma | diffuse B cell MC type | non Hodgkins lymphoma | 20%
|
| anemia | MCC of vitamin B12 deficiency | pernicious anemia | 20%
|
| polycytosis | JAK2 mutation | polycythemia vera | 20%
|
| polycytosis | hyperviscous blood, increased hgb | polycythemia vera | 20%
|
| polycytosis | facial plethora | polycythemia vera | 20%
|
| polycytosis | pruritus after hot bath/shower (2) | polycythemia vera, CML | 20%
|
| anemia | dactylitis | sickle cell anemia | 20%
|
| anemia | howell jolly bodies | sickle cell anemia | 20%
|
| anemia | valine substitution for glutamic acid on beta chain | sickle cell anemia | 20%
|
| anemia | frontal bossing | thalassemia | 20%
|
| anemia | target cells | thalassemia | 20%
|
| anemia | hydrops fetalis | thalassemia | 20%
|
| thrombocytopenia | fever, microangiopathic hemolytic anemia, thrombocytopenia, renal failure, neurological changes | TTP | 20%
|
| anemia | elevated homocysteine (2) | vitamin B12 and B9 deficiency | 20%
|
| anemia | absorbed in the terminal ileum | vitamin B12 deficiency | 20%
|
| anemia | paresthesias, gait abnormalities, memory loss | vitamin B12 deficiency | 20%
|
| anemia | elevated methylmalonic acid | vitamin B12 deficiency | 20%
|
| anemia | positive schilling test | vitamin B12 deficiency | 20%
|
| blood disorder | autosomal dominant disorder (2) | von willebrand's disease, protein c deficiency | 20%
|
| leukemia | overproliferation of immature WBC blasts (2) | AML, ALL | 0%
|
| leukemia | pancytopenia (3) | AML, ALL, CLL | 0%
|
| leukemia | nontender, round and freely mobile, cervical/supraclavicular LAD | CLL | 0%
|
| leukemia | overproliferation of mature granulocytes | CML | 0%
|
| thrombocytopenia | dripping blood | DIC | 0%
|
| thrombophilia | thrombosis, miscarriage | factor v leiden | 0%
|
| thrombocytopenia | normal coagulation studies (2) | Factor V Leiden, TTP | 0%
|
| thrombocytopenia | GP IIb/IIa receptor antibody | ITP | 0%
|
| thrombocytopenia | mucocutaneous bleeding, purpura, petechiae, gingival bleeding | ITP | 0%
|
| myeloma | plasmacytosis > 10% on bone marrow biopsy | multiple myeloma | 0%
|
| myeloma | increased monoclonal Ab | multiple myeloma | 0%
|
| thrombophilia | warfarin-induced skin necrosis | protein C deficiency | 0%
|
| thrombophilia | vitamin K dependent protein deficiency | protein C deficiency | 0%
|
| thrombophilia | purpura fulminans, thrombosis | protein C deficiency | 0%
|
| thrombocytopenia | decreased haptoglobulin | TTP | 0%
|
| thrombocytopenia | MC inherited clotting disorder | von willebrand's disease | 0%
|
| thrombocytopenia | mucocutaneous bleeding, petechiae | von willebrand's disease | 0%
|
| thrombocytopenia | prolonged PTT (3) | von willebrand's disease, hemophilia A, hemophilia B | 0%
|